Full article

Renato VW Bach, Ricardo V Carvalho, Alberto R Gonçalves e Carlos Humberto Vicuña

Abstract

Purpose: to report on a rare case of Caroli’s disease presented as an hepatic exophytic mass. Methods: the authors reviewed the literature about Caroli’s disease and its forms of presentation, and report an atypical case of the disease.
Results: Caroli’s disease is characterized by a segmental and sacular dilatation of intrahepatic biliary ducts. We report an atypical case of the disease, presented as an hepatic exophytic mass on a 3-year-old female child. We have resected the mass and the patient is asymptomatic after a 33-month follow-up.
Conclusions: Caroli’s disease is a differential diagnosis to hepatic exophytic masses.

Key words: Caroli’s disease; liver neoplasms; diagnostic; child.