 Vol.48
n° 2
Artigo completo
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Splenic
haemangioma and Kasabach-Merritt Syndrome as differential diagnosis for
abdominal mass in a newborn: case report
Hemangioma esplênico e Síndrome de Kasabach-Merritt como
diagnóstico diferencial de massa abdominal do recém-nascido
RVW Bach,1 RV Carvalho,2 PAS Faria,3 AR Gonçalves1 e CHV Mariño1
Abstract
We report a rare case of splenic haemangioma in the form of an abdominal
mass in a 20-day-old female newborn with coagulopathy and thrombocytopenia.
She was operated on, and the mass was found to be a tumor of the inferior
pole of the spleen. She remains well after six months of follow-up. The
diagnostic and treatment options are reviewed and discussed. The authors
reviewed the literature about splenic haemangioma in newborns, noticing
that it is the third reported case associating splenic haemangioma and
Kasabach-Merritt Syndrome. Splenic haemangioma is a rare differential
diagnosis to abdominal masses in newborns.
Haemangioma is the most frequent benign neoplasm of the spleen. Anemia,
thrombocytopenia and coagulopathy are often found in patients with large
cavernous haemangioma associated with Kasabach-Merritt syndrome (KMS).
The development of splenic haemangiomas in that syndrome is extremely
rare in newborns.
Key words: hemangioma; splenic neoplasms; abdominal masses; newborn
tumors; therapy; diagnostic; newborn infant.
1Pós-graduando da Seção de Cirurgia Pediátrica.
Instituto Nacional de Câncer, Hospital do Câncer I, Rio
de Janeiro, RJ - Brasil.
2Médico Cirurgião Pediátrico da Seção
de Cirurgia Pediátrica. Instituto Nacional de Câncer, Hospital
do Câncer I, Rio de Janeiro, RJ - Brasil.
3Médico Patologista da Seção de Anatomopatologia.
Instituto Nacional de Câncer, Hospital do Câncer I, Rio
de Janeiro, RJ - Brasil.
4Médico Cirurgião Pediátrico, Chefe da Seção
de Cirurgia Pediátrica. Instituto Nacional de Câncer, Hospital
do Câncer I, Rio de Janeiro, RJ - Brasil. Enviar correspondência
para A.R.G. E-mail: albertog@inca.gov.br
Recebido em maio de 2001
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